Giant Congenital Sialolipoma of Parotid Gland with Parapharyngeal Extension

Document Type : Case Report


1 Department of Otorhinolaryngology, Dokuz Eylül University School of Medicine, Izmir, Turkey.

2 Department of Radiology, Dokuz Eylül University School of Medicine, Izmir, Turkey.

3 Department of Pathology, Dokuz Eylül University School of Medicine, Izmir, Turkey.


Sialolipoma is an extremely rare salivary gland tumor characterized by a well circumscribed mass composed of glandular tissue and mature adipose elements. Herein our aim was to present the fifth case of congenital sialolipoma, which was firstly followed up as a parotid gland hemangioma, and underline the fact that sialolipomas should be kept in mind in the differential diagnosis of congenital parotid gland masses.
Case Report:
A 10-month old male presented with a left-sided huge neck mass which progressed after birth. Radiologic examination revealed a tumor originating from the parotid gland filling the parapharyngeal space. Histopathologic examination of an incisional biopsy was consistent with sialolipoma. A total parotidectomy with preservation of the facial nerve was performed at the age of 1 year. The postoperative recovery was uneventful with normal facial nerve function. There was no recurrence at the 24-month follow-up.
Although it is a very rare benign tumor, congenital sialolipoma should be kept in mind in the differential diagnosis of congenital parotid mass.


Main Subjects

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