Iranian Journal of Otorhinolaryngology

Iranian Journal of Otorhinolaryngology

Pseudotumor of the Maxillary Sinus in a Child with Von Willebrand Disease

Document Type : Case Report

Authors
Martha Lucía Gutierrez Perez 1
Juan Antonio Lugo Machado 2
Natalia Barreto Nino 1
Luis Alfonso Paredes Bastos 1
David Fernando Acevedo Contreras 1
1 Medical Doctor. Universidad El Bosque, Colombian School of Medicine, Otorhinolaryngology Interest Group UEB (ORLIG-UEB), Bogotá, Colombia.
2 Departement of Otorhinolaryngology Head and Neck Surgery, Hospital General de Obregón, Sonora, Secretaria de Salubridad y Asistencia, Ciudad Obregón, Sonora, México.
10.22038/ijorl.2022.58284.3004
Abstract
Introduction:
Mandibular pseudotumors, also known as blood cysts, are rare complications which occur more frequently in patients with an associated bleeding disorder such as hemophilia.
Case Report:
We present a case of a 2-year and 6-month-old patient with a hemophilic pseudotumor associated with Von Willebrand's disease, who consulted the emergency room due to spontaneous increase in volume of the left maxillary region, with no previous relevant medical history.
Conclusions:
Different imaging studies were carried out to characterize the lesion, providing the necessary information for the correct approach. Due to the low prevalence of this complication, we believe it is of vital importance to understand the adequate management in this patient population.
Keywords
Child
Hemophilic pseudotumor
Mandibular diseases
Pediatrics
Von Willebrand diseases
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Iranian Journal of Otorhinolaryngology
Volume 34, Issue 6
November and December 2022
Pages 333-336