Multifocal Langerhans' Cell Histiocytosis in an Adult

Document Type : Case Report

Authors

1 Sinus and Surgical Endoscopic Research Center, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran.

2 Department of Pathology , Faculty of Medicine ,Mashhad university of medical sciences , Mashhad ,Iran.

Abstract

Introduction:
Multifocal Langerhans' cell histocytosis is a rare condition that can affect multiple organs and manifest in various scenarios. While the condition is more commonly found in children, it can also occur in adults.
Case Report:
A 43-year-old female presented with refractory otorrhea and had a rubbery neck mass in the left mid-cervical area, as well as an itchy eczematoid lesion in the left parietal area. The otic lesion was eventually resected, and histopathologic examination confirmed the diagnosis of Langerhans histiocytosis.
Conclusions:
Although rare in adults, Langerhans histiocytosis should be considered as one of the differential diagnoses for ear canal polyps. If diagnosed, medical treatment should be pursued.
 

Keywords

Main Subjects

References

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Iranian Journal of Otorhinolaryngology
Volume 35, Issue 4
July and August 2023
Pages 227-230

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