Huge Facial Desmoid Tumors with Neck Extension: A Case Report

Document Type : Case Report

Authors

1 Department of Otorhinolaryngology, Jondishapour University of Medical Sciences, Ahwaz, Iran.

2 Department of Otorhinolaryngology, Damascus University of Medical Sciences, Damascus, Syria.

3 Department Oral and maxillofacial surgery, Damascus University of Medical Sciences, Damascus, Syria.

Abstract

Introduction:
Desmoid tumors are very rare, benign fibrous neoplasms arise from the musculoaponeurotic structures throughout the body.
 
Case Report:
The patient was a   seven-year old boy with a large mandibular mass growing over a period of six months. His CT-scan showed a large mass, 13 cm in diameter in the cheek area extending to the neck and trachea. Biopsy was compatible with desmoid fibromatosis.  He was given neoadjovant treatment with vinblastin and methotrexate. The patient underwent a tracheostomy. Then a complete hemimandibulectomy and submandibular gland excision was performed.  Finally reconstruction with latisimus dorsi free flap was performed.
 
Conclusion:
Despite rarity desmoid tumors should be kept in mind of an otorhinolaryngologist as a differential diagnosis in children with head and neck mass.
 

Keywords

References

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Iranian Journal of Otorhinolaryngology
Volume 26, Issue 3 - Serial Number 3
July and August 2014
Pages 191-194

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