ntroduction: Sublingual dermoid cysts are rare and constitute a little percent of all dermoid cysts. Typically, these cysts present as a non-painful slow growing mass floor of the mouth or submental region. They can cause problems in deglution, speech and respiration. These lesions can be diagnosed by ultrasonography, CT or MRI. Surgical excision is the treatment of choice, which can be done through extra- or intra- oral approach. We report case of a large sublingual dermoid cyst in a 17 years old girl, who was referred to hospital because of sublingual mass, submental swelling and fibrovascular lesions of lower face.