Polymorphous Low Grade Adenocarcinoma of the Parotid in a Teenager

Document Type : Case Report

Authors

1 Department of Radiotherapy, Government Medical College and Hospital, Chandigarh, India.

2 Department of Otorhinolaryngology and Head and Neck Surgery, Government Medical College and Hospital, Chandigarh, India.

3 Department of Pathology, Government Medical College and Hospital, Chandigarh, India.

Abstract

Abstract
Introduction:
Polymorphous low grade adenocarcinoma (PLGA) is a rare salivary gland neoplasm with an indolent course. It occurs primarily in the minor salivary glands but can rarely occur in the major salivary glands. It usually occurs in the fifth to seventh decades of life with female preponderance.
 
Case Report:
A 16-year-old male presented with recurrent painless swelling in the right preauricular region and with a history of surgical intervention at the same site in the past. His histopathology report was suggestive of pleomorphic adenoma. The swelling recurred after one year of excision and a superficial parotidectomy was performed. The detailed histopathological examination was suggestive of Polymorphous low grade adenocarcinoma. In view of close margins, the patient was given adjuvant radiotherapy. Thirty-three months post-surgery, he is alive and disease-free. We describe a rare case of PLGA of the parotid gland in a teenager with its clinical characteristics, histopathological features, and treatment.
 
Conclusion:
The occurrence of PLGA in the parotid gland is rare with only a few cases reported in literature. The diagnosis of PLGA is challenging due to morphological diversity.

Keywords

Main Subjects

References

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Iranian Journal of Otorhinolaryngology
Volume 29, Issue 5 - Serial Number 94
September and October 2017
Pages 299-302

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