Embryonal Rhabdomyosarcoma - A Mimicker of Squamosal Otitis Media

Document Type : Case Report

Authors

1 Department of Otorhinolaryngology, Kasturba Medical College, Manipal Academy of Higher Education Madhavnagar Manipal - 576104.

2 Department of Pathology, Kasturba Medical College, Manipal Academy of Higher Education Manipal.

Abstract

Introduction:
Rhabdomyosarcoma is the most frequently occurring intrusive soft tissue sarcoma in the pediatric age group. Orbit is the most common location for a pediatric rhabdomyosarcoma, but it can occur in the oral cavity, pharynx, face and neck in the descending order of incidence. Rhabdomyosarcoma in the ear is extremely rare.
 
Case Report:
A 5-year-old girl presented to the outpatient department of our tertiary care hospital with complaints of foul smelling, non-blood stained right ear discharge of one-month duration and deviation of angle of mouth to the left side of acute onset. Investigations revealed a diagnosis of embryonal rhabdomyosarcoma. Multimodal therapy was carried out, and the child was rendered disease-free after two years.
 
Conclusion:
Embryonal rhabdomyosarcoma of the head and neck mimics chronic otitis media. Early diagnosis is essential to deliver prompt treatment and prevent locoregional spread and metastasis.

Keywords

References

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Iranian Journal of Otorhinolaryngology
Volume 32, Issue 1 - Serial Number 108
January and February 2020
Pages 57-61

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