Otoscleroma of the Middle Ear and Mastoid Cavity with Facial Palsy: A Case Report

Document Type : Case Report

Authors

1 Department of Otorhinolaryngology, Faculty of Medicine, Alexandria University, Egypt.

2 Department of Pathology, Faculty of Medicine, Alexandria University, Egypt.

10.22038/ijorl.2024.79380.3675

Abstract

Introduction:
Scleroma is a chronic, specific granulomatous disease that affects the head and neck mucosa. Its common sites are the nose and larynx; however, it might affect other areas. One of the rare sites to be affected is the middle ear and mastoid cavity, for which the term otoscleroma was coined. We present such a rare case in this report.
 
Case Report:
A 47-year-old patient with a history of both old laryngoscleroma and recent Rhinoscleroma. He presented with symptoms of ear discharge and facial palsy. Examination revealed complete facial nerve palsy and an external auditory canal polyp. A decision was made to perform subtotal petrosectomy with facial nerve decompression and maximum debulking to be sent for histopathology. The result came typical of otoscleroma
 
Conclusion:
Otoscleroma is a fairly rare occurrence. It might be primary, with no evidence of Scleroma in other sites or following rhino and/or laryngoscleroma. It might be unilateral or bilateral. It might mimic the clinical picture of chronic suppurative otitis media and its complications. Tympano-mastoidectomy is recommended to stop the discharge, obtain a proper biopsy and decompress the facial nerve if needed. Otoscleroma should be suspected in the case of previous Scleroma in other sites, and otitis media or complications like manifestations.
 

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  1. Olson GW: Scleroma, resume of literatures. Ann OtoI59:186, 1950
  2. Scott-Brown WG: Diseases of the Ear, Nose and Throat. London, Butterworths, 1965,p.214.

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

  1. Shaw HI, Martin H: Rhinoscleroma. J Laryng 75:1011,1961
  2. Badrawi R: Dacryoscleroma. Ann Otol 71:247, 1962.
  3. Von Hebra F: Meber ein Cigenthum liches Neugebilde Naserhinoskelerom. Wien Med Wchnschr 20:1-5, 1870
  4. Yassin A, Safwat F: Unusual features of scleroma. P Laryng and Stol 80:524, 1966
  5. Mossallam, I. and Attia, D.M. (1956): Primary scleroma of the maxillary sinus, Journal of Egypt Medical Association, 39: 512.
  6. Goravalingappa JP, Belagavi CS. Scleroma of the middle ear. Indian J Otolaryngol 1980; 32(1):21.
  7. Brescia MA, Tartaglione EF: Scleroma neonatorum. J Pediat 45:6,1954
  8. Quevedo J: Scleroma in Guatemala. Ann OtoI58:613-645, 1949
  9. Abou-Bieh A, Bedawy AE-f. Otoscleroma. J Laryngol Otol 1975; 89(5):545-8.
  10. Barbary A, Fouad H, Fatt-Hi A. Scleroma Affecting the Middle Ear Cavity with Report of Three Cases. Ann Otol Rhinol Laryngol 1974; 83(1):107-10.
  11. 13-Kakeri AR, Patel AH. A rare case of primary otoscleroma of the middle ear. J Laryngol Otol 2012; 126(12):1276-7.
  12. 14-MAWSON, S. R. (1963) Diseases of the Ear, 1st Edition. London: Edward Arnold, P-38.